| Autoimmune pancreatitis (AIP) is a special type of pancreatitis, and is because of autoimmune mechanism. Recently
published International Consensus Diagnostic Criteria for Autoimmune Pancreatitis include Guidelines of the International Association of
Pancreatology, classifying AIP into types 1 and 2, using five cardinal features of AIP, namely imaging of pancreatic parenchyma and
duct, serology, other organ involvement, pancreatic histology, and an optional criterion of response to steroid therapy. Extrapancreatic
presentations can include sclerosing cholangitis, retroperitoneal fibrosis, sclerosing sialadenitis, lymphadenopathy, nephritis, and
interstitial pneumonia. Extrapancreatic lesions could be synchronously or metachronously diagnosed with AIP, sharing the same
pathological conditions, showing also a favorable result to corticosteroid therapy and distinct differentiation between IgG4-related
diseases fromthe inherent lesions of the corresponding organs. In this article we will review this area mainly based on data fromabroad. |
