| 李佳丹 田洪榛 陈江 陈光辉.成人弯刀综合症1 例并相关文献复习[J].,2014,14(11):2126-2128 |
| 成人弯刀综合症1 例并相关文献复习 |
| Scimitar Syndrome of an Adult: A case Report and Review of Literature |
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| DOI： |
| 中文关键词: 弯刀综合症 先天性心肺血管疾病 成年 诊断 |
| 英文关键词: Scimitar Syndrome Congenital cardio-pulmonary vascular disease Adult Dignosis |
| 基金项目:国家高技术研究发展计划（2011AA020101） |
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| 中文摘要: |
| 目的：探讨我院1 例成人弯刀综合症患者的临床表现、诊断手段及治疗方法。方法：简要陈述我院1 例成人弯刀综合症患
者的入院基本情况及诊疗过程，调研并结合相关文献进行复习。结果：该患者结合临床表现，通过超声心动图、胸部后前位X 片及
右心导管造影等检查，结果证实该患者右下肺静脉畸形引流，诊断为弯刀综合症，并进行相关对症治疗及后续生活和治疗指导。
结论：弯刀综合症为一种罕见而复杂的先天性心肺血管疾病，属于肺静脉畸形引流的一个类型(心下型)，病因不明，此病在成人中
更为少见，该病的诊断主要依赖于右心导管术和心血管造影以及一些影像学手段，成人型多以保守对症治疗为主，若出现严重症
状者则选择外科手术纠正畸形引流治疗。 |
| 英文摘要: |
| Objective: To study the clinical manifestation, diagnosis and treatment of Scimitar Syndrome.Methods: Basic
conditions and the teatment process of one case diagnosed with Scimitar Syndrome were briefly described，and its relevant literatures
were surveyed and reviewed. Results:Right inferior anomalous pulmonary venous was confirmed by ultrasound、plain chest radiographs
and angiocardiography combined with clinical manifestations，and Scimitar Syndrome was diognosed. She wad accepted symptomatic
treatment and guidance of follow-up life. Conclusion:Scimitar syndrome is a rare and complex congenital cardio-pulmonary vascular
disease,and one type of anomalous pulmonary venous drainage (infracardiac type). Its etiology is unclear. The disease is more rare in
adults.Its diagnosis is mainly dependent onangiocardiography and imaging methods. The adult combined with Scimitar Syndrome are
usually given symptomatic treatment. If severe symptoms appearsIts primary treatment is surgery to correct anonialous drainage. |
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